Question 1

What is the nutrition goal used for patients aged 2-20 years who have cystic fibrosis? A) Weight at the 50^th percentile for age B) Height at the 50^th percentile for age C) BMI at the 50^th percentile for age D) Weight for length at the 50^th percentile for age

Accepted Answer

The nutrition goal for patients aged 2-20 years with cystic fibrosis is to maintain a BMI at or above the 50th percentile for age to ensure adequate growth and nutritional status.

Question 2

What is the maximum recommended meal dose for enzymes for patient with cystic fibrosis?&#10;A) 500 units lipase/kg/meal&#10;B) 1000 units lipase/kg/meal&#10;C) 2000 units lipase/kg/meal&#10;D) 2500 units lipase/kg/meal

Accepted Answer

The maximum recommended meal dose for pancreatic enzyme replacement therapy in cystic fibrosis patients is 2500 units of lipase per kilogram per meal to prevent fibrosing colonopathy and ensure effective digestion.

Question 3

Which of the following meets diagnostic criteria for CF-related diabetes?&#10;A) OGTT 2-hour glucose >200 mg/dL&#10;B) OGTT 2-hour glucose >140 mg/dL&#10;C) Random blood glucose >150 mg/dL&#10;D) Fasting blood glucose >120 mg/dL

Accepted Answer

CF-related diabetes is diagnosed with an OGTT 2-hour glucose level greater than 200 mg/dL, similar to the criteria for diagnosing diabetes in the general population.

Question 4

What is the recommended amount of salt supplementation for infants <6 months with cystic fibrosis?&#10;A) 1/8 teaspoon daily&#10;B) &#188; teaspoon daily&#10;C) &#189; teaspoon daily&#10;D) 1 teaspoon daily

Accepted Answer

Salt supplementation for infants <6 months with cystic fibrosis is recommended to be 1/8 teaspoon daily.

Question 5

What places infants at an increased risk for developing BPD?&#10;A) Prematurity&#10;B) Low birth weight&#10;C) Intrauterine growth restriction&#10;D) All of these

Accepted Answer

All of these factors, including prematurity, low birth weight, and intrauterine growth restriction, contribute to an increased risk of developing bronchopulmonary dysplasia (BPD) in infants.

Question 6

What is one suggested explanation of poor growth in the BPD population?&#10;A) Decreased caloric needs&#10;B) Lower metabolic rate&#10;C) Decreased work of breathing&#10;D) Increased work of breathing

Accepted Answer

Increased work of breathing in individuals with BPD (Bronchopulmonary Dysplasia) leads to higher energy expenditure, which can contribute to poor growth due to the increased caloric needs not being met.

Question 7

_______ more accurately reflects lean body tissue mass and is not influenced by edema.&#10;A) Weight&#10;B) Length&#10;C) Head circumference

Accepted Answer

The answer of _______ more accurately reflects lean body tissue...

Question 8

What are nutrition risks associated with long term oral steroid use?&#10;A) Delayed linear growth&#10;B) Hyperglycemia&#10;C) Obesity&#10;D) Decreased bone density&#10;E) All of these

Accepted Answer

Long-term oral steroid use can lead to delayed growth in children, increased blood sugar levels, weight gain, and reduced bone density, making all options correct.

Question 9

Breast feeding for over 12 months reduces the chances of developing asthma.

Accepted Answer

The answer of Breast feeding for over 12 months reduces...

Question 10

All children with asthma should avoid cow's milk.

Accepted Answer

Not all children with asthma need to avoid cow's milk. Only those with a specific allergy to cow's milk should avoid it, as it can trigger asthma symptoms in those individuals.

Deck 15: Pulmonary Diseases