Deck 17: Neuromuscular Disorders

Question 1

In cases of infant botulism, what treatment reduces time spent on a ventilator and shortens hospital stays

A)Providing human-derived antitoxin botulism immune globulin
B)Antitoxins
C)Antibiotics
D)Nutritional support

Answer 1

A

Question 2

What is the most cited food (approximately 20%) associated with incidences of infant botulism

A)Unsterilized milk
B)Herb-infused oils
C)Home-canned vegetables and fruits
D)Unprocessed honey
E)Corn syrup

Answer 2

D

Question 3

Tetanus affects the respiratory system by causing which of the following symptoms
I)Muscle spasms
II)Muscle rigidity
III)Diaphragmatic dysfunction
IV)Trismus

A)I and II
B)I, II, and IV
C)I, II, III, and IV
D)II, III, and IV

Answer 3

C

Question 4

What are the three types of myasthenia gravis (MG)
I)Congenital MG
II)Neonatal MG
III)Adolescent MG
IV)Juvenile MG
V)Infantile MG

A)I, III, and V
B)II, IV, and V
C)II, III, and V
D)I, II, and IV

Question 5

What is the most lethal X-linked genetic disease that causes rapid muscle weakness

A)Spinal muscular atrophy
B)Limb-girdle muscular dystrophy
C)Duchenne's muscular dystrophy
D)Myasthenia gravis

Question 6

How does a registered respiratory therapist noninvasively track the decline of patients with Guillain Barré syndrome
I)Maximal inspired pressure
II)Minute ventilation
III)Forced vital capacity
IV)Tidal volume
V)Maximal expiratory pressure

A)I, III, and V
B)II, IV, and V
C)I only
D)I and V

Question 7

What is the most Common form of botulism

A)Food-borne botulism
B)Wound-borne botulism
C)Infant-borne botulism D! None of the above

Question 8

What are the registered respiratory therapist's responsibilities in addressing deCompensation in neuromuscular patients
I)Polysomnography study
II)Bronchial hygiene therapy
III)Bronchodilator therapy
IV)Noninvasive ventilation
V)Bedside pulmonary function testing

A)I, III, and V
B)I, II, IV, and V
C)II, III, and V
D)I, II, III, IV, and V

Question 9

Intubation and mechanical ventilation is warranted for a patient diagnosed with Guillain Barré syndrome when vital capacity drops below _____.

A)30 mL/kg
B)20 mL/kg
C)5-10 mL/kg
D)5-7 m/kg

Question 10

Patients with Duchenne's muscular dystrophy should perform which of the following tests to keep a close eye on their pulmonary status
I)Forced vital capacity
II)Room air pulse oximetry
III)Peak Cough flow
IV)Maximum inspired pressure divided by maximal expiratory pressure
V)Capnography
VI)Arterial blood gases

A)I, II, III, IV, and V
B)I, II, III, IV, V, and VI
C)I, III, IV, and VI
D)II, III, IV, V, and VI

Question 11

What disorder causes Compromised airway tone, obstructive apneas, and hypopneas during sleep

A)Spinal muscular atrophy
B)Limb-girdle muscular dystrophy
C)Duchenne's muscular dystrophy
D)Myasthenia gravis

Question 12

What are the best modes of ventilation for patients with Guillain Barré syndrome
I)Synchronized intermittent mechanical ventilation pressure Control
II)Synchronized intermittent mechanical ventilation pressure Control with pressure support
III)Volume ventilation
IV)Volume support ventilation

A)I and III
B)I and IV
C)II and III
D)II and IV

Question 13

What anaerobic bacterium causes tetanus

A)StaphyloCoccus species
B)StreptoCoccus species
C)Enterobacteriacae species
D)MyCobacterium tuberculosis
E)Clostridium tetani

Question 14

What infections may trigger Guillain Barré syndrome
I)Campylobacter jejuni
II)MyCoplasma pneumonia
III)Cytomegalovirus
IV)Epstein-Barr virus
V)Varicella-zoster virus

A)I, III, and V
B)II, IV, and V
C)II, III, IV, and V
D)I, II, III, and IV

Question 15

What test Confirms the diagnosis for Guillain Barré syndrome

A)Complete blood Count
B)Electromyography
C)Polysomnography study
D)Cerebrospinal fluid specimen

Question 16

For patients with Congenital myasthenia gravis, what therapy may prevent sudden respiratory failure or apnea
I)Anticholinesterase therapy
II)Pyridostigmine
III)Steroid therapy
IV)Immunosuppressive agent

A)I and III
B)I and II
C)II and III
D)III and IV

Question 17

Typically, what is the first symptom to signal the presence of botulism in an infant

A)Loss of gag reflex
B)Weak suck effort
C)Constipation followed by impaired function of cranial nerves
D)Weak cry
E)Loss of head Control

Question 18

What are the major causes of morbidity and mortality in patients with a neuromuscular disorder

A)Respiratory Complications and ventilator failure
B)Apnea episodes and a decline in pulmonary function tests leading to pulmonary Complications
C)Infections as a result of poor skin integrity
D)Diabetes mellitus and cardiovascular diseases

Question 19

As clinical manifestations of Guillain Barré syndrome progress, all of the following symptoms will be present except: I.Tachycardia
II)Tachypnea
III)Retractions
IV)Normal breath sounds
V)Shortness of breath
VI)Hypoxia

A)I, IV, and V
B)II, III, and VI
C)I, II, III, and VI
D)II, IV, and V

Question 20

Presence of what neuromuscular disorder appears on a radiograph as a classic bell-shaped chest wall

A)Spinal muscular atrophy type 1
B)Spinal muscular atrophy type 2
C)Spinal muscular atrophy type 3
D)Duchenne's muscular dystrophy
E)Limb-girdle muscular dystrophy F.Myasthenia gravis

Question 21

In postoperative patients with Duchenne's muscular dystrophy, what respiratory Complication can arise as result of the respiratory muscle weakness and weak Cough effort
I)Respiratory deCompensation
II)Pneumothorax
III)Atelectasis
IV)Pulmonary edema
V)MuCous plugging

A)I, II, and III
B)I, II, III, IV, and V
C)II, IV, and V
D)I, III, and V

Question 22

Incidences of juvenile myasthenia gravis are more prevalent in Asian populations than in Caucasian populations.

Question 23

Neonatal myasthenia gravis Corrects and resolves within 2 to 4 weeks of onset of symptoms.

Question 24

Patients with a neuromuscular disease are no more prone to developing sColiosis of the spine than are other patients.

Question 25

When should initiation of noninvasive ventilation be Considered in patients with Duchenne's muscular dystrophy
I)Forced vital capacity is less than 50% predicted.
II)Abnormal sleep study suggesting hypoventilation and hypercarbia
III)SpO₂ is less than 95% while awake.
IV)Maximal expiratory pressure is less than 40 cm H₂O.

A)I and II
B)I, III, IV
C)II and III
D)I, II, III, IV