Deck 41: Cystic Fibrosis

Question 1

MATCHING
The clinical scenarios associated with respiratory disease result from the pathophysiologic mechanisms caused (or activated) by the anatomic alterations of the lungs associated with the disorder. Using the "Yes" or "No" items, match the major anatomic alterations of the lungs that cause the clinical scenario associated with Cystic Fibrosis.
Excessive Bronchial Secretions Clinical Scenario

A)YES-This is associated with cystic fibrosis.
B)NO-This is not associated with cystic fibrosis.

Answer 1

YES-This is associated with cystic fibrosis.

Question 2

Next to the pulmonary function studies listed, match the findings listed below that typically develop in patients with cystic fibrosis. Items may be used once, more than once, or not at all.
FRC

A)Normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Answer 2

Increases

Question 3

MATCHING
The clinical scenarios associated with respiratory disease result from the pathophysiologic mechanisms caused (or activated) by the anatomic alterations of the lungs associated with the disorder. Using the "Yes" or "No" items, match the major anatomic alterations of the lungs that cause the clinical scenario associated with Cystic Fibrosis.
Increased Alveolar-Capillary Membrane Thickness Clinical Scenario

A)YES-This is associated with cystic fibrosis.
B)NO-This is not associated with cystic fibrosis.

Answer 3

NO-This is not associated with cystic fibrosis.

Question 4

Next to the pulmonary function studies listed, match the findings listed below that typically develop in patients with cystic fibrosis. Items may be used once, more than once, or not at all.
FEV_T

A)Normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 5

Next to the pulmonary function studies listed, match the findings listed below that typically develop in patients with cystic fibrosis. Items may be used once, more than once, or not at all.
ERV

A)Normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 6

Next to the pulmonary function studies listed, match the findings listed below that typically develop in patients with cystic fibrosis. Items may be used once, more than once, or not at all.
VC

A)Normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 7

Next to the pulmonary function studies listed, match the findings listed below that typically develop in patients with cystic fibrosis. Items may be used once, more than once, or not at all.
FEF_50%

A)Normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 8

Next to the pulmonary function studies listed, match the findings listed below that typically develop in patients with cystic fibrosis. Items may be used once, more than once, or not at all.
FVC

A)Normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 9

Next to the pulmonary function studies listed, match the findings listed below that typically develop in patients with cystic fibrosis. Items may be used once, more than once, or not at all.
TLC

A)Normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 10

Next to the pulmonary function studies listed, match the findings listed below that typically develop in patients with cystic fibrosis. Items may be used once, more than once, or not at all.
V_T

A)Normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 11

MATCHING
The clinical scenarios associated with respiratory disease result from the pathophysiologic mechanisms caused (or activated) by the anatomic alterations of the lungs associated with the disorder. Using the "Yes" or "No" items, match the major anatomic alterations of the lungs that cause the clinical scenario associated with Cystic Fibrosis.
Alveolar Consolidation Clinical Scenario

A)YES-This is associated with cystic fibrosis.
B)NO-This is not associated with cystic fibrosis.

Question 12

Next to the pulmonary function studies listed, match the findings listed below that typically develop in patients with cystic fibrosis. Items may be used once, more than once, or not at all.
RV

A)Normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 13

MATCHING
The clinical scenarios associated with respiratory disease result from the pathophysiologic mechanisms caused (or activated) by the anatomic alterations of the lungs associated with the disorder. Using the "Yes" or "No" items, match the major anatomic alterations of the lungs that cause the clinical scenario associated with Cystic Fibrosis.
Atelectasis Clinical Scenario

A)YES-This is associated with cystic fibrosis.
B)NO-This is not associated with cystic fibrosis.

Question 14

Next to the pulmonary function studies listed, match the findings listed below that typically develop in patients with cystic fibrosis. Items may be used once, more than once, or not at all.
MVV

A)Normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 15

Next to the pulmonary function studies listed, match the findings listed below that typically develop in patients with cystic fibrosis. Items may be used once, more than once, or not at all.
FEF _200-1200

A)Normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 16

MATCHING
The clinical scenarios associated with respiratory disease result from the pathophysiologic mechanisms caused (or activated) by the anatomic alterations of the lungs associated with the disorder. Using the "Yes" or "No" items, match the major anatomic alterations of the lungs that cause the clinical scenario associated with Cystic Fibrosis.
Distal Airway and Alveolar Weakening Clinical Scenario

A)YES-This is associated with cystic fibrosis.
B)NO-This is not associated with cystic fibrosis.

Question 17

MATCHING
The clinical scenarios associated with respiratory disease result from the pathophysiologic mechanisms caused (or activated) by the anatomic alterations of the lungs associated with the disorder. Using the "Yes" or "No" items, match the major anatomic alterations of the lungs that cause the clinical scenario associated with Cystic Fibrosis.
Bronchospasm Clinical Scenario

A)YES-This is associated with cystic fibrosis.
B)NO-This is not associated with cystic fibrosis.

Question 18

Next to the pulmonary function studies listed, match the findings listed below that typically develop in patients with cystic fibrosis. Items may be used once, more than once, or not at all.
PEFR

A)Normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 19

Next to the pulmonary function studies listed, match the findings listed below that typically develop in patients with cystic fibrosis. Items may be used once, more than once, or not at all.
FEF _25%-75%

A)Normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 20

Next to the pulmonary function studies listed, match the findings listed below that typically develop in patients with cystic fibrosis. Items may be used once, more than once, or not at all.
IC

A)Normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 21

Match what arterial blood gas changes occur during severe cystic fibrosis with the items below. Items may be used once, more than once, or not at all.
pH

A)Increases
B)Decreases
C)Normal

Question 22

Match what develops in the oxygen indices of patients with cystic fibrosis to the items listed below. Items may be used once, more than once, or not at all.
C(a-v)

A)Remains normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 23

Match what arterial blood gas changes occur during severe cystic fibrosis with the items below. Items may be used once, more than once, or not at all.
HCO₃^-

A)Increases
B)Decreases
C)Normal

Question 24

Next to the pulmonary function studies listed, match the findings listed below that typically develop in patients with cystic fibrosis. Items may be used once, more than once, or not at all.
RV/TLC ratio

A)Normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 25

Match what hemodynamic indices develop during the severe stages of cystic fibrosis to the items listed below. Items may be used once, more than once, or not at all.
CO

A)Normal
B)Decreases
C)Increases

Question 26

Match what hemodynamic indices develop during the severe stages of cystic fibrosis to the items listed below. Items may be used once, more than once, or not at all.
PCWP

A)Normal
B)Decreases
C)Increases

Question 27

Match what arterial blood gas changes occur during mild to moderate cystic fibrosis with the items below. Items may be used once, more than once, or not at all.
pH

A)Increases
B)Decreases
C)Normal

Question 28

Match what arterial blood gas changes occur during mild to moderate cystic fibrosis with the items below. Items may be used once, more than once, or not at all.
PaCO₂

A)Increases
B)Decreases
C)Normal

Question 29

Match what hemodynamic indices develop during the severe stages of cystic fibrosis to the items listed below. Items may be used once, more than once, or not at all.
PA

A)Normal
B)Decreases
C)Increases

Question 30

Match what develops in the oxygen indices of patients with cystic fibrosis to the items listed below. Items may be used once, more than once, or not at all.
O₂ER

A)Remains normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 31

Match what hemodynamic indices develop during the severe stages of cystic fibrosis to the items listed below. Items may be used once, more than once, or not at all.
CVP

A)Normal
B)Decreases
C)Increases

Question 32

Match what develops in the oxygen indices of patients with cystic fibrosis to the items listed below. Items may be used once, more than once, or not at all.
O₂

A)Remains normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 33

Match what arterial blood gas changes occur during mild to moderate cystic fibrosis with the items below. Items may be used once, more than once, or not at all.
HCO₃^-

A)Increases
B)Decreases
C)Normal

Question 34

Match what hemodynamic indices develop during the severe stages of cystic fibrosis to the items listed below. Items may be used once, more than once, or not at all.
RAP

A)Normal
B)Decreases
C)Increases

Question 35

Match what hemodynamic indices develop during the severe stages of cystic fibrosis to the items listed below. Items may be used once, more than once, or not at all.
SV

A)Normal
B)Decreases
C)Increases

Question 36

Match what develops in the oxygen indices of patients with cystic fibrosis to the items listed below. Items may be used once, more than once, or not at all.
DO₂

A)Remains normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 37

Next to the pulmonary function studies listed, match the findings listed below that typically develop in patients with cystic fibrosis. Items may be used once, more than once, or not at all.
FEV_1%

A)Normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 38

Match what arterial blood gas changes occur during severe cystic fibrosis with the items below. Items may be used once, more than once, or not at all.
PaCO₂

A)Increases
B)Decreases
C)Normal

Question 39

Match what develops in the oxygen indices of patients with cystic fibrosis to the items listed below. Items may be used once, more than once, or not at all.
SvO₂

A)Remains normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 40

Match what develops in the oxygen indices of patients with cystic fibrosis to the items listed below. Items may be used once, more than once, or not at all.
_S/ _T

A)Remains normal
B)Decreases
C)Increases
D)Normal or decreased
E)Normal or increased

Question 41

Match what hemodynamic indices develop during the severe stages of cystic fibrosis to the items listed below. Items may be used once, more than once, or not at all.
RVSWI

A)Normal
B)Decreases
C)Increases

Question 42

Under normal circumstances, every cell in the body (except the sex cells) has how many chromosomes?

A) 16
B) 23
C) 46
D) 92

Question 43

Match what hemodynamic indices develop during the severe stages of cystic fibrosis to the items listed below. Items may be used once, more than once, or not at all.
SVR

A)Normal
B)Decreases
C)Increases

Question 44

Patients with cystic fibrosis commonly demonstrate a decreased RV.

Question 45

Which of the following is/are commonly cultured from the mucus in the tracheobronchial tree of the patient with cystic fibrosis?

A) I and III only
B) II and IV only
C) I, II, and III only
D) II, III, and IV only

Question 46

An elevated hemoglobin concentration is associated with the advanced stages of cystic fibrosis.

Question 47

Match what hemodynamic indices develop during the severe stages of cystic fibrosis to the items listed below. Items may be used once, more than once, or not at all.
CI

A)Normal
B)Decreases
C)Increases

Question 48

During the advanced stages of cystic fibrosis, the patient generally demonstrates diminished breath sounds.

Question 49

Match what hemodynamic indices develop during the severe stages of cystic fibrosis to the items listed below. Items may be used once, more than once, or not at all.
PVR

A)Normal
B)Decreases
C)Increases

Question 50

Match what hemodynamic indices develop during the severe stages of cystic fibrosis to the items listed below. Items may be used once, more than once, or not at all.
SVI

A)Normal
B)Decreases
C)Increases

Question 51

Match what hemodynamic indices develop during the severe stages of cystic fibrosis to the items listed below. Items may be used once, more than once, or not at all.
LVSWI

A)Normal
B)Decreases
C)Increases

Question 52

When two carriers of the cystic fibrosis gene produce children, there is a 25% chance that the baby will have cystic fibrosis.

Question 53

Both Haemophilus influenzae and Pseudomonas aeruginosa are commonly found in the tracheobronchial tree secretions of patients with cystic fibrosis.