Which of the following is the deficient enzyme in glycogen storage disease Ia (GSD Ia)?

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GSD Ia involves a defect in the enzyme glucose-1,6-phosphatase.This defect results in impairments in gluconeogenesis and glycogenolysis, which can result in severe hypoglycemia.Fructose-1,6-diphosphatase deficiency is a rare fructose metabolism disorder that promotes metabolic acidosis when fructose is consumed, but fructose levels do not increase in the blood or urine.Hereditary fructose intolerance is associated with a defect in fructose-1-phosphate aldolase that causes a depletion of inorganic phosphate and adenosine triphosphate.This disorder can result in renal and liver damage.Metabolic disorders involving hexokinase have not been identified.

Which of the Following Is the Deficient Enzyme in Glycogen