A 2-year-old child who only just arrived in the country with his family is taken to the office because he is agitated and cries a lot. Although the mother's pregnancy went without a hitch, the patient had to be delivered by cesarean section because of an obstructed labor. According to his mother, he has progressed less quickly than his brother in terms of being able to lift his head, crawl, and walk. Additionally, she has noted that the patient's skull is bigger than that of other kids her age. He is 50th percentile in height, 60th percentile in weight, and 95th percentile in head circumference. The picture below shows a head CT scan. Which of the following is the most likely diagnosis?

Question

A 2-year-old child who only just arrived in the country with his family is taken to the office because he is agitated and cries a lot. Although the mother's pregnancy went without a hitch, the patient had to be delivered by cesarean section because of an obstructed labor. According to his mother, he has progressed less quickly than his brother in terms of being able to lift his head, crawl, and walk. Additionally, she has noted that the patient's skull is bigger than that of other kids her age. He is 50th percentile in height, 60th percentile in weight, and 95th percentile in head circumference. The picture below shows a head CT scan.  Which of the following is the most likely diagnosis?

Quizplus · Accepted Answer

Eductional Objective: Dandy-Walker malformation is a developmental anomaly characterized by hypoplasia/absence of the cerebellar vermis and cystic dilation of the fourth ventricle with posterior fossa enlargement.  Patients often present during infancy with developmental delay and progressive skull enlargement.  Other features may include cerebellar dysfunction and non-communicating hydrocephalus

A 2-Year-Old Child Who Only Just Arrived in the Country