Children with phenylketonuria have to replace approximately 80% of _____ intake from foods with a mixture of _____ from which phenylalanine has been removed.

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Children with phenylketonuria have a deficiency in the enzyme phenylalanine hydroxylase, which prevents the metabolism of the amino acid phenylalanine. This can lead to a buildup of phenylalanine in the body, which is toxic to the brain and can cause developmental delays and intellectual disability. Therefore, they need to replace most of their protein intake from foods with a special formula that contains all the essential amino acids except for phenylalanine. This formula is called a protein substitute, and it provides the necessary nutrients for growth and development without causing any harm.

Children with Phenylketonuria Have to Replace Approximately 80% of _____