An 8-month-old child with congenital myotonic dystrophy has been hospitalized with a severe respiratory infection.Which action by the nurse is the most appropriate?

Question

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Congenital myotonic dystrophy usually causes death before the age of 1 year due to the inability to maintain respirations.In this situation,the nurse should have a meeting with the family to explore a broad range of therapeutic options,including palliative care measures and code status.Just inquiring about ventilatory support is too narrow a focus.Lung transplantation is not a treatment for this disorder.Children with this disease die at a young age,and so they do not grow up dependent on ventilators.

An 8-Month-Old Child with Congenital Myotonic Dystrophy Has Been Hospitalized