A peripheral blood smear of a patient reveals many giant platelets.Platelet function tests all show normal aggregation with the exception of ristocetin.From what is the patient most likely suffering?

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Bernard-Soulier syndrome is characterized by giant platelets and abnormal ristocetin-induced platelet aggregation. It is an inherited disorder caused by a mutation in one of the genes coding for the glycoprotein Ib-V-IX complex, which is essential for platelet adhesion to injured vessels. Glanzmann's thrombasthenia, on the other hand, is also a rare inherited bleeding disorder, but it is characterized by a lack of platelet aggregation due to deficiency or dysfunction of the glycoprotein IIb/IIIa complex, which is necessary for platelet-to-platelet interactions. Storage pool disease and Wiskott-Aldrich syndrome are also inherited platelet disorders, but they have different clinical and laboratory features than Bernard-Soulier syndrome.

A Peripheral Blood Smear of a Patient Reveals Many Giant