Which disorder affecting the jaw bones and facies is characterized by fusion of the anterior portion of the maxillary gingiva to the upper lip from canine to canine?

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Ellis-van Creveld syndrome is characterized by fusion of the anterior portion of the maxillary gingiva to the upper lip from canine to canine. This syndrome has an autosomal-recessive inheritance pattern. The gene for this syndrome has been mapped to the short arm of chromosome 4 region 16. Gardner syndrome is characterized by the presence of osteomas in various bones, especially the frontal bones, mandible, and maxilla. Mandibulofacial dysostosis is characterized by a facies with downward sloping of the palpebral fissures, a hypoplastic nose, hypoplastic malar bones with hypoplasia or absence of the zygomatic process, abnormal and misplaced ears, and a receding chin. Cherubism is characterized by a progressive bilateral facial swelling that appears when the patient is between 2 and 4 years of age.

Which Disorder Affecting the Jaw Bones and Facies Is Characterized