Which syndrome is characterized by intestinal polyps, which become malignant at age 30 and after?

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Gardner syndrome is characterized by intestinal polyps, which become malignant at age 30 and after. It is also known as familial colorectal polyposis. Polyposis primarily affects the colon and rectum and generally develops before puberty. Some authors recommend intestinal resection when the polyps appear because their malignant transformation into adenocarcinoma is invariable, especially with increasing age. Osteogenesis imperfecta is characterized by defective collagen and results in abnormally formed bones that fracture easily. Nevoid basal cell carcinoma syndrome is characterized by mild hypertelorism and mild prognathism, with frontal and parietal enlargement and a broad nasal root. Mandibulofacial dysostosis is characterized by a mouth that appears fishlike, with downward sloping of the lip commissures. The facies shows downward sloping of the palpebral fissures, a hypoplastic nose, hypoplastic malar bones with hypoplasia or absence of the zygomatic process, abnormal and misplaced ears, and a receding chin.

Which Syndrome Is Characterized by Intestinal Polyps, Which Become Malignant