A patient with _____ will have a mouth that appears fishlike, with downward sloping of the lip commissures.

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A patient with mandibulofacial dysostosis will have a mouth that appears fishlike, with downward sloping of the lip commissures. The facies shows downward sloping of the palpebral fissures, a hypoplastic nose, hypoplastic malar bones with hypoplasia or absence of the zygomatic process, abnormal and misplaced ears, and a receding chin. The lower eyelids show a cleft of the outer third, with a lack of lashes medial to it. The ears may exhibit tags, which on occasion can also be seen near the angle of the mouth. Osteogenesis imperfecta is characterized by a dentinogenesis imperfecta-like condition. Primary teeth are affected in 80% of patients, whereas permanent teeth are affected in only 35% of these individuals. The crowns, roots, and pulp chambers are generally smaller than normal. Cherubism is characterized by radiographs of the jaws that show a typical "soap-bubble" or multilocular appearance, which usually occupies the ascending ramus of the mandible and extends into the molar and premolar areas. Cleidocranial dysplasia is characterized by a premaxilla that is generally underdeveloped, resulting in pseudoprognathism. These patients have many supernumerary teeth, sometimes even simulating a third dentition.

A Patient with _____ Will Have a Mouth That Appears