A platelet release defect in which there is a severe deficiency of dense granules in platelets is known as:

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Hermansky-Pudlak syndrome is a rare genetic disorder characterized by decreased platelet aggregation due to the severe deficiency of dense granules in platelets. Other symptoms may also include albinism, lung and bowel disease, and bleeding disorders. Chediak-Higashi syndrome is a rare genetic disorder that affects the immune and nervous system, causing a decrease in platelet count. Wiskott-Aldrich syndrome is also a rare genetic disorder that causes immunodeficiency and a decrease in platelet count. Bernard-Soulier syndrome is a rare genetic disorder that causes thrombocytopenia and impaired platelet function due to a deficiency in the glycoprotein Ib-IX-V complex.

A Platelet Release Defect in Which There Is a Severe