All of the following are characteristics of phenylketonuria EXCEPT:

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Phenylketonuria is a genetic disorder characterized by a deficiency or defect in phenylalanine hydroxylase, which leads to the accumulation of phenylalanine and its byproduct phenylpyruvate in the body. Excretion of phenylpyruvate is one of the diagnostic features of phenylketonuria. Patients with untreated phenylketonuria may suffer severe mental retardation, which is why the condition is often detected early and managed by putting the patient on a diet low in phenylalanine. However, air oxidation causing urine to turn dark on standing is not a characteristic feature of phenylketonuria.

All of the Following Are Characteristics of Phenylketonuria EXCEPT