Which of the following urea cycle enzyme deficiencies is inherited as an X-linked dominant trait that is usually lethal in males?

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Ornithine transcarbamylase deficiency is an X-linked dominant trait. Males with this deficiency usually die within the first few days of life. Females who inherit the mutation can have variable symptoms depending on the degree of X-inactivation in affected tissues. Ornithine transcarbamylase deficiency is an X-linked dominant trait that is usually lethal in males. The other options (A, B, D) are all inherited in an autosomal recessive manner.

Which of the Following Urea Cycle Enzyme Deficiencies Is Inherited