While performing an assessment on a child, you notice that the child's urine has a sweet odor. Testing confirms the presence of maple syrup urine disease. What is the appropriate treatment for this metabolic disorder?

Question

Quizplus · Accepted Answer

Maple syrup urine disease is treated with dietary management and sometimes large doses of thiamine, as it can help in some cases where the enzyme deficiency is responsive to thiamine.

While Performing an Assessment on a Child, You Notice That