Characteristic urine odors are associated with all of the following disorders except:
A) Alkaptonuria
B) PKU
C) Maple syrup urine disease
D) Isovaleric acidemia

Question

Quizplus · Accepted Answer

Alkaptonuria is characterized by the accumulation of homogentisic acid, leading to darkening of urine upon standing, but it does not typically cause a distinctive odor like the other conditions listed. PKU, Maple syrup urine disease, and Isovaleric acidemia are metabolic disorders that can lead to characteristic urine odors due to the accumulation of specific substances.

Characteristic Urine Odors Are Associated with All of the Following