Neurofibromatosis of von Recklinghausen is characterized by

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Neurofibromatosis of von Recklinghausen is characterized by café au lait pigmentation of the skin in 90% of patients. Multiple neurofibromas, which appear as papules and growths of various sizes, are seen on the facial skin, especially the eyelids. Malignant transformation of the neurofibromas occurs in an estimated 3% to 15% of patients with neurofibromatosis. Oral involvement is seen in about 10% of patients and is characterized by single or multiple tumors at any location in the oral mucosa, the most frequent being the lateral borders of the tongue.

Neurofibromatosis of Von Recklinghausen Is Characterized by