Which of the following is a rare inherited congenital disorder that results in large amounts of UPG I accumulating in the RBCs, bone marrow, and urine of these patients due to an abnormal pathway for the synthesis of protoporphyrin?

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Erythropoietic porphyria, also known as congenital erythropoietic porphyria (CEP), is a rare inherited congenital disorder that results in large amounts of uroporphyrinogen I accumulating in the RBCs, bone marrow, and urine of these patients due to an abnormal pathway for the synthesis of protoporphyrin. Ringed sideroblastic anemia is a disorder that affects the production of heme in the body. Hepatic porphyria is a group of disorders that affect the liver's ability to produce heme. Thalassemia is a group of inherited disorders that affect the production of hemoglobin.

Which of the Following Is a Rare Inherited Congenital Disorder